4457 3-Mercaptolactate-cysteine disulfide 3-mercaptolactate-cysteine disulfide is a compound analog of cysteine excreted in the urine of patients affected by Mercaptolactate-cysteine disulfiduria (MCDU, OMIM 249650), the product of disorder of sulfur amino acid metabolism and a reduced activity of the enzyme mercaptopyruvate sulfurtransferase (MST, EC 2.8.1.2). Reduction of protein in the diet, addition of pyridoxine or of neomycin did not affect the urinary excretion of beta-mercaptolactate-cysteine disulfide of a mentally defective patient who was excreting this mixed disulfide. Addition of cysteine to the diet did increase the excretion of this disulfide (A3477, A3478, A3479, A3480). 18841-42-4 193536 C6H11NO5S2 White powder. No indication of carcinogenicity to humans (not listed by IARC). This is an endogenously produced metabolite found in the human body. It is used in metabolic reactions, catabolic reactions or waste generation. 2014-08-29T06:50:59Z 2026-04-06T12:17:21Z true N[C@@H](CSSCC(O)C(O)=O)C(O)=O C6H11NO5S2 InChI=1S/C6H11NO5S2/c7-3(5(9)10)1-13-14-2-4(8)6(11)12/h3-4,8H,1-2,7H2,(H,9,10)(H,11,12)/t3-,4?/m0/s1 MAFDYIDMXCXBRB-WUCPZUCCSA-N 241.285 241.007863847 Endogenous Solid HMDB06512 167948 Kobayashi, Kanji; Ikegami, Takuma; Ubuka, Toshihiko. New metabolites of cystine. II. Chemical and biochemical properties of S-(2-oxo-2-carboxyethylthio)cysteine. Physiological Chemistry and Physics (1973), 5(2), 167-71. CHEM003363 NS00123372 120.84999999999998 53.21430000000001 22.105696041289708 7 6 4 1.6834861757602564 9.040677528575356 -1 0 -3.08 -0.93 2.83e+01 g/l